In Sturge-Weber syndrome, what is one of the potential surgical interventions?

Sturge-Weber syndrome is a neurocutaneous disorder characterized by the presence of a facial capillary malformation (port-wine stain), leptomeningeal angiomas, and neurological complications such as seizures and developmental delays. One of the significant manifestations of this syndrome is focal cortical dysplasia, which can lead to refractory epilepsy.

In cases where patients with Sturge-Weber syndrome experience uncontrollable seizures that do not respond to medical treatment, a surgical intervention might be warranted. Focal cerebral resection of the affected lobe can be considered as a treatment option. This procedure aims to remove the area of the brain where the seizures originate, which is often located in the lobe of the brain adjacent to the leptomeningeal angioma. By excising the affected tissue, it can significantly reduce or even eliminate seizure activity, improving the patient’s quality of life.

The other surgical options listed do not address the underlying issues associated with Sturge-Weber syndrome. Craniotomy for tumor removal is not relevant here, as Sturge-Weber involves vascular malformations rather than tumors. Cerebellar decompression is more appropriate for conditions involving increased intracranial pressure or specific cerebellar lesions, rather than the cortical malformations seen in Sturge-We